Arch Hand Microsurg 2018; 23(3): 184-189  
Surgical Treatment of Syndactyly of Harlequin Ichthyosis
Sung Jae Ahn1, Jong Won Hong1,2
1Department of Plastic and Reconstructive Surgery, Yonsei University College of Medicine, Seoul, Korea
2Institute for Human Tissue Restoration, Yonsei University College of Medicine, Seoul, Korea
Correspondence to: Jong Won Hong
Department of Plastic and Reconstructive Surgery, Yonsei University College of Medicine, 50-1 Yonsei-ro, Seodaemun-gu, Seoul 03722, Korea
TEL: +82-2-2228-2225, FAX: +82-2-393-6947, E-mail: saturn@yuhs.ac
Received: April 24, 2018; Revised: May 16, 2018; Accepted: May 28, 2018; Published online: September 1, 2018.
© Korean Society for Surgery of the Hand, Korean Society for Microsurgery, and Korean Society for Surgery of the Peripheral Nerve. All rights reserved.

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
Abstract
Harlequin ichthyosis (HI) is a rare and most severe form of autosomal recessive congenital ichthyoses characterized by excessive hyperkeratosis. The skin anomalies affect the shape of eyes, ears, nose, mouth, and distal extremities. Since HI is very fatal, there is a lack of data that documents successful treatment of HI patients with syndactyly. We successfully managed syndactyly in a HI patient by using a conventional method without any complication and we noticed an improvement functionally and aesthetically.
Keywords: Lamellar ichthyosis, Syndactyly, Hand deformities, Skin transplantation


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